Scholte HR, Rodrigues Pereira R, de Jonge PC, Luyt-Houwen IE, Hedwig M, Verduin M, Ross JD: Primary carnitine deficiency
48,49,50,51 Moreover, through the action of two of the enzymes involved in the production of H 2 Scysteine aminotransferase (CAT) and 3-mercaptopyruvate sulphurtransferase (3-MST)cysteine is sequentially converted into 3-mercaptopyruvate (3-MP) with the release of an amino group that will react with -ketoglutarate, ending with the formation of glutamate and pyruvate (Fig
& Reguiai, Z
Dyachok J, Earnest S, Iturraran EN et al (2016) Amino acids regulate mTORC1 by an obligate two-step mechanism
Certain medications can also lead to a deficiency in carnitine
The immunostained sections were scanned on a NanoZoomer NDP system (Hamamatsu Photonics, Shizuoka, Japan) with 20 resolution, or on a FV3000 confocal microscope (Olympus, Tokyo, Japan) with 4, 10 or 20 resolution